The aim of this study was to evaluate costs of treatment and hospital utilization among patients with hemophilia a and b, with and without inhibitors, over a 3year period in a portuguese comprehensive care hemophilia centre. A short overview of the quality of life construct and its link with health and wellbeing will be addressed. Hemophilia a and b are inherited bleeding disorders characterized by deficiency or dysfunction of. It is caused by a defect in one of the genes that determines how the body makes certain bloodclotting factors. Guidelines for the management of hemophilia 2nd edition prepared by the treatment guidelines working group, on behalf of the world federation of hemophilia wfh dr. See actions taken by the people who manage and post content.
Facebook is showing information to help you better understand the purpose of a page. Congenital hemophilia a and b rare bleeding disorders. For permission to reproduce or translate this document, please contact the. Pdf computer file format was first created in 1993 by. Desmopressin ddavp in the treatment of bleeding disorders. Document managementengineering document format using pdfpart 1. Hemophilia free download as powerpoint presentation. A hemofilia e uma condicao potencialmente incapacitante, cujo tratamento esta. Brewer department of oral surgery, the royal infirmary. Pipettes should preferably be accurate within signifi cantly less than 10%. Diagnosis of hemophilia and other bleeding disorders. This results in people bleeding for a longer time after an injury, easy bruising, and an increased risk of bleeding inside joints or the brain.
A clonagem e o sequenciamento do gene levaram a varias deducoes. Alok srivastava chair department of hematology, christian medical college, vellore, tamil nadu, india dr. O gene do fator viii foi mapeado no braco longo distal do cromossomo x e clonado. Congenital hemophilia is an inherited bleeding disorder characterized by an absent or reduced level of clotting factor viii 8 or factor ix 9. In a person with normal amounts of clotting factors, when bleeding starts, all of the clotting factors work together to form a clot that stops the bleeding. Although hemophilia has a potentially high economic impact, there are no published estimates of healthcare costs for this disease in portugal. Hemophilia is a rare bleeding disorder in which a persons blood does not clot properly. Trastornos hemorragicos, deportes y ejercicio versiones en espanol estaran disponible pronto. Costs and utilization of treatment in patients with hemophilia. If a pipette is inaccurate beyond the following limits mean weight, it must be taken out of use immediately. When clotting factors are missing or your body does not have enough clotting factors, it can. Scribd is the worlds largest social reading and publishing site. Hemofilia dr jorge pena hematologo pediatra hospital pablo tobon uribe definicion. Hemofilia congenita e inibidor biblioteca virtual em saude.
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